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Radiological Evaluation of Cystic Lung Disease

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Diffuse Cystic Lung Diseases

Part of the book series: Respiratory Medicine ((RM))

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Abstract

The diffuse cystic lung diseases (DCLDs) are characterized by the presence of multiple, thin-walled, air-filled spaces in the pulmonary parenchyma. The differential diagnosis for DCLDs is broad and includes congenital, inflammatory, infectious, and neoplastic etiologies as well as cyst mimics such as emphysema and bronchiectasis. The most commonly encountered DCLDs include lymphangioleiomyomatosis (LAM), pulmonary Langerhans cell histiocytosis (PLCH), and lymphoid interstitial pneumonia (LIP). Computed tomography (CT) is recommended to evaluate suspected or known DCLD. Helpful clues for diagnosis include cyst distribution and shape. In addition, ancillary lung and extrapulmonary findings can suggest the diagnosis. Chest CT in conjunction with clinical and laboratory information often allow establishment of the diagnosis without further invasive testing.

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Authors and Affiliations

  1. Department of Radiology, University of Wisconsin School of Medicine and Public Health, Madison, WI, USA

    Joanna E. Kusmirek & Cristopher A. Meyer

  2. Department of Radiology, National Jewish Health, Denver, CO, USA

    David A. Lynch

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  2. Cristopher A. Meyer
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  3. David A. Lynch
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Editors and Affiliations

  1. University of Cincinnati, Cincinnati, OH, USA

    Nishant Gupta

  2. Cincinnati Children’s Hospital Medical Center, Cincinnati, OH, USA

    Kathryn A. Wikenheiser-Brokamp

  3. University of Cincinnati, Cincinnati, OH, USA

    Francis X. McCormack

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Kusmirek, J.E., Meyer, C.A., Lynch, D.A. (2021). Radiological Evaluation of Cystic Lung Disease. In: Gupta, N., Wikenheiser-Brokamp, K.A., McCormack, F.X. (eds) Diffuse Cystic Lung Diseases. Respiratory Medicine. Humana, Cham. https://doi.org/10.1007/978-3-030-63365-3_3

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  • DOI: https://doi.org/10.1007/978-3-030-63365-3_3

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  • Publisher Name: Humana, Cham

  • Print ISBN: 978-3-030-63364-6

  • Online ISBN: 978-3-030-63365-3

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