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Troponin-I elevation in a young man with arrhythmogenic right ventricular dysplasia/cardiomyopathy

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Abstract

Ventricular arrhythmias occur frequently in patients with arrhythmogenic right ventricular dysplasia/cardiomyopathy (ARVD/C) as well as those with ischemic heart disease. We present the case of a 29-year-old man with ARVD/C and multiple episodes of symptomatic ventricular tachycardia terminated by implantable cardioverter defibrillator (ICD) discharges. Phasic elevation of troponin-I prompted repeated coronary angiograms, all of which were normal. The patient was successfully treated with radiofrequency ablation. This case illustrates that ARVD/C may result in elevated cardiac enzymes in the absence of coronary artery disease.

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Authors and Affiliations

  1. Department of Medicine, Johns Hopkins University School of Medicine, 600 North Wolfe Street, Baltimore, MD, 21287, USA

    William J. Kostis & Daniel L. Miller

  2. Department of Medicine, Division of Cardiology, Johns Hopkins University School of Medicine, Baltimore, MD, 21287, USA

    Ryan J. Tedford, Steven P. Schulman & Gordon F. Tomaselli

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  1. William J. Kostis
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  2. Ryan J. Tedford
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  3. Daniel L. Miller
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  4. Steven P. Schulman
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  5. Gordon F. Tomaselli
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Correspondence to William J. Kostis.

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Kostis, W.J., Tedford, R.J., Miller, D.L. et al. Troponin-I elevation in a young man with arrhythmogenic right ventricular dysplasia/cardiomyopathy. J Interv Card Electrophysiol 22, 49–53 (2008). https://doi.org/10.1007/s10840-008-9250-1

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  • DOI: https://doi.org/10.1007/s10840-008-9250-1

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