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Serosal involvement in IgG4-related disease: report of two cases and review of the literature

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Abstract

IgG4-related disease (IgG4-RD) is a recently described entity characterized by lymphoplasmacytic infiltrates, usually mimicking tumors, affecting almost every organ or system. Nevertheless, serosal involvement has been rarely reported. In this article, we report two cases of IgG4-RD with serosal involvement and review the literature. Because of the varied clinical pictures found in our review, we suggest a new terminology for the description of IgG4-RD with serosal involvement.

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Authors and Affiliations

  1. Servicio de Medicina Interna, Hospital Son Llàtzer, Carretera de Manacor Km 4, 07198, Palma, Spain

    Juan González-Moreno, Inés Losada-López, Cristina Gállego-Lezaun & Mercedes García-Gasalla

  2. Pathology Department, Hospital Universitari Son Espases, Palma, Spain

    Cristina Gómez Bellvert

  3. Autoimmune Systemic Disease Unit, Hospital Clínico San Cecilio, Granada, Spain

    Norberto Ortego Centeno

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  1. Juan González-Moreno
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Correspondence to Juan González-Moreno.

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Juan González-Moreno, Inés Losada-López, Critina Gállego-Lezaun, Mercedes García-Gasalla, Cristina Gómez Bellvert, and Norberto Ortego Centeno declare that they have no conflict of interest.

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González-Moreno, J., Losada-López, I., Gállego-Lezaun, C. et al. Serosal involvement in IgG4-related disease: report of two cases and review of the literature. Rheumatol Int 36, 1033–1041 (2016). https://doi.org/10.1007/s00296-016-3501-8

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  • DOI: https://doi.org/10.1007/s00296-016-3501-8

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