Acute splenic sequestration crises in adults with sickle cell disease☆
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Cited by (40)
Splenic sequestration in the adult: cross sectional imaging appearance of an uncommon diagnosis
2021, Clinical ImagingCitation Excerpt :Clinically, splenic sequestration crisis is defined as a drop in hemoglobin level by 2 g/dL in the setting of an enlarging spleen [4]. However, the diagnosis may not always be evident clinically, especially in the adult population in whom this condition is rarely encountered [5]. With regards to imaging, prior reported cases of splenic sequestration have presented at CT and ultrasound with an enlarged spleen and a thick irregular rim of hypoenhancement or hypoechogenicity along the splenic periphery [6–8].
TTP-like syndrome associated with hemoglobin SC disease treated successfully with plasma and red cell exchange
2019, Leukemia Research ReportsCitation Excerpt :The incidence of sickle crisis in HbSC is around 23–36% as per few studies. These patients retain their splenic activity into adulthood making them prone for sequestration crisis [6]. During splenic sequestration, the splenic sinuses become engorged leading to extravascular removal of platelets and erythrocytes.
Hematologic Complications of Pregnancy
2016, Obstetrics: Normal and Problem PregnanciesSickle cell disease: Registry of the Spanish Society of Pediatric Hematology
2006, Anales de PediatriaAcute splenic sequestration: A rare and severe complication of sickle cell anemia in adults. A case report
2005, Revue de Medecine InterneAdverse outcome of acute splenic sequestration crisis in pregnancy
2021, Obstetric Medicine
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This work was supported in part by a grant (HL-15160) from the National Heart, Lung, and Blood Institute, Bethesda, Maryland, and was published in abstract form (Blood 1984; 64 [suppl 1]: 53a.).
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