Double H-type tracheoesophageal fistula

https://doi.org/10.1016/j.epsc.2020.101662Get rights and content
Under a Creative Commons license
open access

Abstract

Congenital ‘isolated’ tracheoesophageal fistula (TEF) is a rare variant of esophageal atresia, also termed H-type TEF. Even rarer is a double H-type TEF. Here, we report a two-week-old female, with double H-type TEF – one identified pre-operatively, the other during surgery. Pre-operative laryngotracheobronchoscopy (LTB) with guidewire cannulation is considered key to definitive TEF repair, to aid in both pre- and intra-operative identification of the fistula(e). In our experience, only one H-type TEF was identified at the planned pre-operative LTB, with the second H-type fistula identified at the time of cervical dissection. Both fistulae were repaired during the same operation, via cervical approach. This represents the first reported case of a double H-type TEF, repaired primarily via a single cervical incision.

Keywords

Tracheoesophageal fistula
Congenital
Case report

Abbreviations

EA
esophageal atresia
GI
gastrointestinal
HRIM
high resolution impedance manometry
LTB
laryngotracheobronchoscopy
TEF
tracheoesophageal fistula
VACTERL
vertebral anomalies anorectal malformations cardiovascular anomalies tracheoesophageal fistula renal anomalies and limb defects

Cited by (0)